History and examination may suggest underlying pathology
Consider the following investigation
Upper GI endoscopy
Barium swallow
Endoscopic ultrasound
Oesophageal manometry
CT or MRI scan
Achalasia
Due to reduced number of ganglion cells in myenteric plexus
Vagi show axonal degeneration of the dorsal motor nucleus and nucleus ambiguous
Aetiology is unknown but a neurotropic virus may be important
Similar to Chagas' disease due to Trypanosoma Cruzi
Clinical features
Commonest in patients between 40 - 70 years
Male : female ratio is approximately equal
Symptoms include dysphagia, weight loss, regurgitation, chest pain
5% of patients develop squamous carci
noma
Investigations
CXR - widening of mediastinum, air / fluid level and absence of gastric fundus gas bubble
Barium Swallow - dilatation & residue, small tertiary contractions and 'rat tail' of distal oesophagus
Manometry - absent primary peristaltic wave and non-propulsive tertiary contractions
Endoscopy - essential to exclude 'pseudoachalasia' due to submucosal carcinoma
Tight lower oesophageal sphincter which relaxes with gentle pressure usually seen
Isotope transit studies
Differential diagnosis
Diffuse oesophageal spasm
Infiltrating carcinoma
Hypertrophic lower oesophageal sphincter
Scleroderma
Chagas' disease
Treatment options
Two treatment options are commonly available
Treatment selected should be based in individual patient needs
Balloon Dilatation
Rider Moeller Balloon
Inflated to 300 mmHg for 3 minutes
3% perforation rate
60% dysphagia free at 5 years
May be repeated if necessary
Cardiomyotomy
Described by Heller (1914) & Grenveldt (1918)
May be performed laparoscopically
85% will have an improvement in symptoms
10% develop oesophageal reflux
3% will develop and oesophageal stricture
Some combine cardiomyotomy with an antireflux operation
Bibliography
Banerjee S. Achalasia of the cardia. Hospital Update Sep 1993. 480 - 488. Hunt D R, Wills V L. Laparoscopic Heller Myotomy for achalasia. Aust NZ J Surg 2000; 70: 582-586. Hunter J G, Richardson W S. Surgical management of achalasia. Surg Clin N Am 1997; 77: 993-1115. Lamb P J, Griffin S M, Beckingham I J. Controversial topics in surgery. Achalasia of the cardia - dilatation or division? Ann R Coll Surg Engl 2006; 88: 9-12 Leslie P, Carding P N, Wilson J A. Investigation and management of chronic dysphagia. Br Med J 2003; 326: 433-436. Navaratnam R M, Clayman C, Winslet M C. Clinical advances in the evaluation of oesophageal disease. Hosp Med 2000; 64: 194-199